{"product_id":"l-carnitine","title":"L-Carnitine","description":"\u003ch2\u003eL-Carnitine\u003c\/h2\u003e\n\u003cp\u003eL-Carnitine (L-3-hydroxy-4-(trimethylammonio)butanoate) is an endogenous quaternary ammonium compound biosynthesised from lysine and methionine in the liver and kidneys, and is an essential cofactor for mitochondrial long-chain fatty acid oxidation. It is one of the most extensively studied metabolic compounds in biochemistry, with well-characterised roles in fatty acid transport, energy metabolism, and mitochondrial function. L-Carnitine is supplied here as a research-grade compound for in vitro and preclinical investigation of fatty acid oxidation, mitochondrial bioenergetics, and carnitine-dependent metabolic pathways.\u003c\/p\u003e\n\u003ch3\u003eMechanism of Action\u003c\/h3\u003e\n\u003cp\u003eL-Carnitine functions as the obligate carrier molecule for the transport of long-chain fatty acyl-CoA esters across the inner mitochondrial membrane via the carnitine palmitoyltransferase (CPT1\/CPT2) shuttle system. In the cytoplasm, CPT1 catalyses the transfer of the acyl group from acyl-CoA to carnitine, forming acylcarnitine, which is then translocated across the inner mitochondrial membrane by the carnitine-acylcarnitine translocase (CACT). Inside the mitochondrial matrix, CPT2 regenerates acyl-CoA for entry into β-oxidation. Without adequate L-carnitine, long-chain fatty acids cannot enter the mitochondrial matrix for oxidation, leading to cytoplasmic lipid accumulation and impaired energy production. L-Carnitine also modulates the acyl-CoA\/CoA ratio, influencing mitochondrial metabolic flexibility and acetyl-CoA availability for the TCA cycle.\u003c\/p\u003e\n\u003ch3\u003eResearch Applications\u003c\/h3\u003e\n\u003cul\u003e\n\u003cli\u003eCPT1\/CPT2 shuttle system and mitochondrial fatty acid transport studies\u003c\/li\u003e\n\u003cli\u003eLong-chain fatty acid β-oxidation and mitochondrial bioenergetics research\u003c\/li\u003e\n\u003cli\u003eCarnitine deficiency, metabolic disease, and lipid accumulation preclinical models\u003c\/li\u003e\n\u003cli\u003eAcyl-CoA\/CoA ratio modulation and mitochondrial metabolic flexibility investigation\u003c\/li\u003e\n\u003cli\u003eExercise metabolism, energy expenditure, and skeletal muscle function research\u003c\/li\u003e\n\u003c\/ul\u003e\n\u003ch3\u003eSpecifications\u003c\/h3\u003e\n\u003cul\u003e\n\u003cli\u003e\n\u003cstrong\u003eMolecular Formula:\u003c\/strong\u003e \u003cmeta charset=\"utf-8\"\u003e\n\u003cspan class=\"T286Pc\" data-sfc-cp=\"\" data-sfc-root=\"ep\" data-sfc-cb=\"\" data-complete=\"true\" data-copy-service-computed-style='font-family: \"Google Sans\", Arial, sans-serif; font-size: 16px; font-weight: 400; margin: 0px; text-decoration: none; border-bottom: 0px rgb(230, 232, 240);'\u003eC₇H₁₅NO₃\u003c!--TgQPHd||[]--\u003e\u003c\/span\u003e\u003c!--TgQPHd||[]--\u003e\n\u003c\/li\u003e\n\u003cli\u003e\n\u003cstrong\u003eMolecular Weight:\u003c\/strong\u003e 161.2 g\/mol\u003c\/li\u003e\n\u003cli\u003e\n\u003cstrong\u003eCAS Number:\u003c\/strong\u003e 541-15-1\u003c\/li\u003e\n\u003cli\u003e\n\u003cstrong\u003ePurity:\u003c\/strong\u003e ≥98%\u003c\/li\u003e\n\u003cli\u003e\n\u003cstrong\u003eForm:\u003c\/strong\u003e Lyophilised powder\u003c\/li\u003e\n\u003cli\u003e\n\u003cstrong\u003eStorage:\u003c\/strong\u003e -20°C\u003c\/li\u003e\n\u003cli\u003e\n\u003cstrong\u003eShelf Life:\u003c\/strong\u003e 24 months\u003c\/li\u003e\n\u003c\/ul\u003e\n\u003cp\u003e\u003cem\u003eThis product is intended for legitimate laboratory and analytical research use only. Not for diagnostic, therapeutic, or consumer use.\u003c\/em\u003e\u003c\/p\u003e","brand":"Vanta Labs","offers":[{"title":"600mg \/ 10mL","offer_id":58103429005576,"sku":"LCAR-600MG","price":19.5,"currency_code":"GBP","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/1049\/8886\/8872\/files\/Vanta_Lab_L-Carnitine.png?v=1783027862","url":"https:\/\/vantalabsuk.com\/products\/l-carnitine","provider":"Vanta Labs","version":"1.0","type":"link"}